REGγ is essential to maintain bone homeostasis by degrading TRAF6, preventing osteoporosis

Proc Natl Acad Sci U S A. 2024 Nov 19;121(47):e2405265121. doi: 10.1073/pnas.2405265121. Epub 2024 Nov 13.

Abstract

Primary osteoporosis, manifesting as decreased bone mass and increased bone fragility, is a "silent disease" that is often ignored until a bone breaks. Accordingly, it is urgent to develop reliable biomarkers and novel therapeutic strategies for osteoporosis treatment. Here, we identified REGγ as a potential biomarker of osteoporotic populations through proteomics analysis. Next, we demonstrated that REGγ deficiency increased osteoclast activity and triggered bone mass loss in REGγ knockout (KO) and bone marrow-derive macrophage (BMM)-conditional REGγ KO mice. However, the osteoclast activity decreased in BMM-conditional REGγ overexpression mice. Mechanistically, we defined that REGγ-20S proteasome directly degraded TRAF6 to inhibit bone absorption in a ubiquitin-independent pathway. More importantly, BMM-conditional Traf6 KO with REGγ KO mice could "rescue" the osteoporosis phenotypes. Based on NIP30 (a REGγ "inhibitor") dephosphorylation by CKII inhibition activated the ubiquitin-independent degradation of TRAF6, we selected TTP22, an inhibitor of CKII, and defined that TTP22 could alleviate osteoporosis in vitro and in vivo. Overall, our study reveals a unique function of NIP30/REGγ/TRAF6 axis in osteoporosis and provides a potential therapeutic drug TTP22 for osteoporosis.

Keywords: NIP30; REGγ; TRAF6; osteoporosis; ubiquitin-independent degradation.

MeSH terms

  • Animals
  • Autoantigens / genetics
  • Autoantigens / metabolism
  • Bone and Bones / metabolism
  • Bone and Bones / pathology
  • Female
  • Homeostasis
  • Humans
  • Macrophages / metabolism
  • Mice
  • Mice, Knockout*
  • Osteoclasts* / metabolism
  • Osteoporosis* / genetics
  • Osteoporosis* / metabolism
  • Osteoporosis* / prevention & control
  • Proteasome Endopeptidase Complex / metabolism
  • Proteolysis
  • TNF Receptor-Associated Factor 6* / genetics
  • TNF Receptor-Associated Factor 6* / metabolism

Substances

  • TNF Receptor-Associated Factor 6
  • Ki antigen
  • TRAF6 protein, mouse
  • Autoantigens
  • Proteasome Endopeptidase Complex