Pathology of Hodgkin's disease

Curr Opin Oncol. 1994 Sep;6(5):456-63. doi: 10.1097/00001622-199409000-00002.

Abstract

This review addresses several current questions about Hodgkin's disease (HD): 1) Does HD represent a single disease or multiple diseases? 2) What is the role of cytokines in HD? 3) What is the nature of the Reed-Sternberg cell? 4) How are Epstein-Barr virus (EBV) and oncogenes (bcl-2, c-myc, and p53) involved in the pathogenesis of HD? Nodular lymphocyte predominance HD appears to be a distinct clinicopathologic entity. Cytokines attract inflammatory cells, induce fibrosis, upregulate oncogenes and adhesion molecules, cause systemic symptoms, and mediate immune suppression. Reed-Sternberg cells are derived from B and T lymphocytes in most instances, although an alternative origin from a follicular dendritic reticulum cell has been proposed. EBV is an etiologic agent in some but not all HD cases. EBV gene products confer a growth advantage on Reed-Sternberg cells. The bcl-2 and p53 oncogenes protect Reed-Sternberg cells from apoptosis and are not directly upregulated by EBV.

Publication types

  • Review

MeSH terms

  • Cytokines / physiology
  • Gene Expression Regulation, Neoplastic
  • Herpesvirus 4, Human / isolation & purification
  • Hodgkin Disease / genetics
  • Hodgkin Disease / immunology
  • Hodgkin Disease / pathology*
  • Hodgkin Disease / virology
  • Humans
  • Oncogenes / genetics
  • Reed-Sternberg Cells / physiology

Substances

  • Cytokines