A male infant with stenosis of the left pulmonary veins and atrial septal defect is reported. He began to have repeated pulmonary infections, with poor response to medical treatment, when he was 6 months old. Localized stenosis of the left upper and lower pulmonary veins were diagnosed with cardiac catheterization at the age of 7 months. Transvenous balloon dilation was attempted, but failed. Surgical treatment with pericardial patch venoplasty of the left pulmonary veins and closure of the atrial septal defect successfully released the pulmonary venous obstruction. There has been a follow-up for more than one year, and no cardiopulmonary symptoms were reported.