Genomic PCR detects tumor cells in peripheral blood from patients with myxoid liposarcoma

Genes Chromosomes Cancer. 1996 Oct;17(2):102-7. doi: 10.1002/(SICI)1098-2264(199610)17:2<102::AID-GCC5>3.0.CO;2-9.

Abstract

Myxoid liposarcoma (MLS) is the most common subtype of liposarcoma. The cytogenetic hallmark of MLS is the pathognomonic t(12;16)(q13;p11), present in more than 85% of cases. The translocation leads to the fusion of the CHOP and FUS genes at 12q13 and 16p11, respectively, and the generation of a FUS/CHOP hybrid protein. The presence of a tumor-specific chimeric gene makes it possible to identify MLS cells by polymerase chain reaction (PCR). We have analyzed peripheral blood samples obtained during a 10-year period at diagnosis of primary and/or recurrent disease in 19 MLS patients with t(12;16) and in one MLS patient with t(12;22;20), resulting in the fusion of the CHOP and EWS genes. Nested PCR on genomic DNA from blood samples amplified FUS/CHOP hybrid fragments in three patients and EWS/CHOP in the patient with t(12;22;20). There was no obvious association between PCR findings and clinical outcome, but larger series are needed to draw any firm conclusions.

Publication types

  • Research Support, Non-U.S. Gov't

MeSH terms

  • Adult
  • CCAAT-Enhancer-Binding Proteins*
  • Chromosomes, Human, Pair 12* / genetics
  • DNA, Neoplasm / analysis*
  • DNA, Neoplasm / blood
  • DNA-Binding Proteins / genetics
  • Female
  • Heterogeneous-Nuclear Ribonucleoproteins
  • Humans
  • Liposarcoma, Myxoid / blood
  • Liposarcoma, Myxoid / genetics*
  • Male
  • Middle Aged
  • Neoplasm Proteins / genetics*
  • Polymerase Chain Reaction
  • RNA-Binding Protein EWS
  • RNA-Binding Protein FUS
  • Ribonucleoproteins / genetics
  • Transcription Factor CHOP
  • Transcription Factors / genetics
  • Translocation, Genetic* / genetics

Substances

  • CCAAT-Enhancer-Binding Proteins
  • DDIT3 protein, human
  • DNA, Neoplasm
  • DNA-Binding Proteins
  • Heterogeneous-Nuclear Ribonucleoproteins
  • Neoplasm Proteins
  • RNA-Binding Protein EWS
  • RNA-Binding Protein FUS
  • Ribonucleoproteins
  • Transcription Factors
  • Transcription Factor CHOP