Peripheral deletion of rheumatoid factor B cells after abortive activation by IgG

Proc Natl Acad Sci U S A. 1997 Jan 21;94(2):646-51. doi: 10.1073/pnas.94.2.646.

Abstract

Rheumatoid factor (RF) B cells proliferate during secondary immune responses to immune complexed antigen and antigen specific T cells, but higher affinity RFs are not detected except in patients with rheumatoid arthritis and other autoimmune diseases. Consequently, there must exist highly efficient mechanisms for inactivation of these higher-affinity RF B cell clones under normal circumstances. Exposure of transgenic mice expressing a human IgM RF to soluble human IgG in the absence of T cell help causes antigen specific B cell deletion in 2-3 days. The deletion is independent of the Fas/Fas ligand (FasL) pathway of apoptosis and is preceded by a phase of partial activation involving increase in cell size and expression of B7 and ICAM-1, and transient release of low levels of immunoglobulin. Complete B cell activation involving the formation of germinal centers and sustained high level RF secretion only occurs if T cell help is provided simultaneously. RF B cells exposed to tolerogen remain competent to secrete RF in vitro if provided with an appropriate antigenic stimulus and T cell help. Consequently, death of these cells is not preceded by anergy. Abortive activation/deletion of B cells by antigen in the absence of T cell-derived survival signals may represent the major mechanism for maintaining peripheral tolerance in B cells expressing higher affinity RF. The lack of anergy, and the potential for reactivation before death, provide a means for maintaining RF production under pathologic circumstances, such as may occur in the inflamed rheumatoid synovium.

Publication types

  • Research Support, Non-U.S. Gov't
  • Research Support, U.S. Gov't, P.H.S.

MeSH terms

  • Animals
  • Apoptosis
  • B-Lymphocytes / immunology*
  • Humans
  • Immune Tolerance
  • Immunoglobulin G / chemistry
  • Immunoglobulin G / immunology*
  • Immunoglobulin M / metabolism
  • Lymphocyte Activation
  • Lymphocyte Depletion
  • Mice
  • Mice, Transgenic
  • Receptors, Antigen, B-Cell / metabolism
  • Rheumatoid Factor / immunology*
  • Solubility

Substances

  • Immunoglobulin G
  • Immunoglobulin M
  • Receptors, Antigen, B-Cell
  • Rheumatoid Factor